- 抗体类型:单克隆
- 抗体来源:小鼠
- 抗体应用:ELISA, WB, IHC, IF
- 特异性:Human; other species not tested.
产品详情
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产品名称
Alpha galactosidase A antibody
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抗体类型
单克隆
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抗体来源
小鼠
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抗体亚型
小鼠IgG2a
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抗体描述
Alpha galactosidase A Mouse Monoclonal antibody. Positive WB detected in HeLa cells, HEK-293 cells, HepG2 cells, human kidney tissue. Positive IF detected in HepG2 cells. Positive IHC detected in human kidney tissue, human liver tissue. Observed molecular weight by Western-blot: 49 kDa
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抗体应用
ELISA, WB, IHC, IF
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应用推荐
Recommended Dilution:
WB: 1:500-1:5000
IHC: 1:20-1:200
IF: 1:20-1:200
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特异性
Human; other species not tested.
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蛋白别名
Alpha galactosidase A, galactosidase, alpha
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制备方法
This antibody was obtained by immunization of Alpha galactosidase A recombinant protein (Accession Number: NM_000169). Purification method: Protein A purified.
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组分
PBS with 0.02% sodium azide and 50% glycerol pH 7.3.
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储存方法
Store at -20℃. DO NOT ALIQUOT
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背景介绍
GLA, also named as Melibiase, Agalsidas and Alpha-galactosidase A, Belongs to the glycosyl hydrolase 27 family. It hydrolysis of terminal, non-reducing alpha-D-galactose residues in alpha-D-galactosides, including galactose oligosaccharides, galactomannans and galactolipids. Fabry disease is an X-linked lysosomal storage disorder resulting from the deficient activity of GLA. Enzyme replacement therapy (ERT) with GLA is currently the most effective therapeutic strategy for patients with Fabry disease, a lysosomal storage disease.