- 抗体类型:单克隆
- 抗体来源:小鼠
- 抗体应用:ELISA, WB, IHC, IF
- 特异性:Human,Mouse; other species not tested.
产品详情
-
产品名称
HADHA antibody
-
抗体类型
单克隆
-
抗体来源
小鼠
-
抗体亚型
小鼠IgG1
-
抗体描述
HADHA Mouse Monoclonal antibody. Positive WB detected in A375 cells, HepG2 cells, Jurkat cells. Positive IHC detected in human heart tissue, human liver tissue. Positive IF detected in HepG2 cells. Observed molecular weight by Western-blot: 79 kDa
-
抗体应用
ELISA, WB, IHC, IF
-
应用推荐
Recommended Dilution:
WB: 1:500-1:5000
IHC: 1:20-1:200
IF: 1:50-1:500
-
特异性
Human,Mouse; other species not tested.
-
蛋白别名
78 kDa gastrin binding protein, ECHA, HADH, HADHA, LCHAD, MTPA, TP ALPHA
-
制备方法
This antibody was obtained by immunization of HADHA recombinant protein (Accession Number: NM_000182). Purification method: Protein G purified.
-
组分
PBS with 0.02% sodium azide and 50% glycerol pH 7.3.
-
储存方法
Store at -20℃. DO NOT ALIQUOT
-
背景介绍
HADHA(Trifunctional enzyme subunit alpha, mitochondrial) is also named as HADH,78 kDa gastrin-binding protein.It belongs to the enoyl-CoA hydratase/isomerase family in the N-terminal section and the 3-hydroxyacyl-CoA dehydrogenase family in the central section.It harbors the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities.Defects in HADHA are a cause of trifunctional protein deficiency (TFP deficiency) and long-chain 3-hydroxyl-CoA dehydrogenase deficiency (LCHAD deficiency) and maternal acute fatty liver of pregnancy (AFLP).
-
参考文献
- <